肉瘤型肾细胞癌是一种罕见的高级别恶性肿瘤，预后较差。我们描述了一个患有小的（最大直径为1.8厘米）肉瘤型透明细胞肾细胞癌和广泛转移的患者的68Ga-FAPI-04 PET/CT检查结果。原发性肾肿瘤和与之相应的骨骼、淋巴结、肾上腺和肝脏转移瘤均显示出增强的68Ga-FAPI-04摄取。原发性肾肿瘤在增强CT上表现出低血管性，类似乳头状肾细胞癌。该案例表明FAPI PET/CT可能对检测和分期这种罕见的恶性肿瘤有用。 版权所有©2023 Wolters Kluwer Health，Inc. 保留所有权利。

Sarcomatoid renal cell carcinoma is an uncommon high-grade malignancy with poor prognosis. We describe 68Ga-FAPI-04 PET/CT findings in a patient with a small (1.8 cm in the maximum diameter) sarcomatoid clear cell renal cell carcinoma with widespread metastatic disease. Both the primary renal tumor and its metastases in bones, lymph nodes, adrenals, and liver showed increased 68Ga-FAPI-04 uptake. The primary renal tumor showed hypovascularity on contrast-enhanced CT, mimicking papillary renal cell carcinoma. This case indicates FAPI PET/CT may be useful for detecting and staging of this unusual malignancy.Copyright © 2023 Wolters Kluwer Health, Inc. All rights reserved.