肉瘤是一类错杂的间充质恶性肿瘤，最常发生在四肢、腹膜后和头颈部位。腹腔内表现罕见，当出现腹膜肉瘤时，治疗特别困难。由于该疾病的总体预后较差，因此需要量身定制的外科治疗方案，以实现有限的发病率并取得满意的预后。我们在医院手术治疗了19例伴有腹膜肉瘤的肉瘤患者，介绍了围手术期和长期预后。回顾了治疗路径并进行了临床随访。对患者特征、病史、肿瘤亚型、手术方法、住院时间、并发症、随访和总体生存率进行了评估。我们的患者中有9名女性和10名男性，中位年龄为45.9岁（18-88），中位生存期为30个月（0-200）。在大多数情况下，腹膜肉瘤是在手术中发现的，或者手术一开始就是为缓解症状而进行的。在这些情况下，手术方法非常不同，应考虑各种因素，为每个患者量身定制治疗方案。分享我们的经验将有助于增加对这种罕见疾病的了解，并为管理未来的病例提供见解。

Sarcomas represent a heterogeneous group of mesenchymal malignancies that most commonly occur in the extremities, retroperitoneum, and head and neck. Intra-abdominal manifestations are rare and prove particularly difficult to treat when peritoneal sarcomatosis is present. Because of the overall poor prognosis of the disease, a tailored approach to surgical management is essential to achieve satisfactory outcomes with limited morbidity. We present the perioperative and long-term outcomes of 19 cases of sarcoma with peritoneal sarcomatosis treated surgically at our hospital. Treatment pathways were reviewed and clinical follow-up was performed. Patient characteristics, medical history, tumor subtype, surgical approach, hospital stay, complications, follow-up, and overall survival (OS) were assessed. Our patients were 9 women and 10 men with a median age of 45.9 years (18-88) and a median survival of 30 months (0-200). In most cases, peritoneal sarcomatosis was either discovered during surgery or the procedure was performed with palliative intent from the beginning. The surgical approach in these cases is very heterogeneous and should consider a variety of factors to tailor an approach for each patient. Sharing our experiences will help to increase knowledge about this rare disease and provide insight into the management of future cases.