牙本质类鬼细胞瘤是一种罕见的良性肿瘤，占所有病例的不到3％，由星状网状组织组成，包括釉质上皮样和基础细胞。尽管牙本质类鬼细胞瘤是一种良性肿瘤，但局部浸润牙源性上皮或复发已被报道，并且其详细的病理学和治疗仍不清楚。本报告描述了一名60岁的日本男性被诊断为上颌牙本质类鬼细胞瘤的病例。图像显示局限性、多房性囊肿病变，内部有钙化物质。为防止病变扩展，进行了造口术和活组织检查，并在初始检查后2年进行了部分上颌切除术。组织病理学的发现显示包含鬼细胞和牙本质oid物质的珐琅质瘤样增生，导致牙本质类鬼细胞瘤的诊断。本文还回顾了最近报道的牙本质类鬼细胞瘤病例。由于可能出现复发，因此进行造口术、适当切除和术后随访非常重要。©2023.作者。

Dentinogenic ghost cell tumor is a rare benign tumor that accounts for less than 3% of all cases and consists of the stellate reticulum, which is made up of enamel epithelioid and basaloid cells. Although DGCT is a benign tumor, the local infiltration of the odontogenic epithelium or recurrences have been reported, and its detailed pathology and treatments remain unclear.This report describes the case of a 60-year-old Japanese male diagnosed with a maxillary dentinogenic ghost cell tumor. Images showed well-circumscribed, multilocular cystic lesions with a calcified substance in the interior. Marsupialization was performed along with biopsy to prevent the expansion of the lesion, and a partial maxillectomy was performed 2 years after the initial examination. Histopathological findings showed ameloblastomatous proliferation containing clusters of ghost cells and dentinoid materials, resulting in the diagnosis of dentinogenic ghost cell tumor. This article also reviews recently reported cases of dentinogenic ghost cell tumor.It is important to perform marsupialization, proper resection, and postoperative follow-up because of possible recurrence.© 2023. The Author(s).