迷走神经副神经节瘤是一种罕见的肿瘤，占头颈部肿瘤的0.03%。这些肿瘤通常位于舌骨的头侧，仅有一例先前报道的病例来源于颈部下三分之一。我们描述了第二例报道的颈部下段迷走神经副神经节瘤的病例，该病例经限制性胸骨切口进行外科进入和切除。一名66岁的男性患者出现颈胸连接处长期存在的病变。CT、MRI和Ga-68 DOTATATE PET / CT显示，在C6到大约T4水平之间，出现一个呈亲和性增强的5.2×4.2×11.5cm肿块。细胞穿刺活检证实了诊断。患者接受导管造影和经直接穿刺技术栓塞术，然后通过联合颈部切口和限制性胸骨切口进行肿块切除。我们描述了一例在颈胸连接处伴有胸骨后方扩展的迷走神经副神经节瘤的不寻常病例，需要通过胸骨切口进行外科切除。 © 2023 Wiley Periodicals LLC.

Vagus nerve paragangliomas are rare tumors, comprising 0.03% of head and neck neoplasms. These tumors are usually located cephalad to the hyoid bone, and there is only one previously reported case that arose from the lower third of the neck.We describe the second reported case of a lower neck vagus nerve paraganglioma that was managed with a limited sternotomy for access and surgical removal.A 66-year-old male presented with a long-standing lesion of the cervicothoracic junction. CT, MRI, and Ga-68 DOTATATE PET/CT showed an avidly enhancing 5.2 × 4.2 × 11.5 cm mass extending from C6 to approximately T4 level. FNA confirmed the diagnosis. The patient underwent catheter angiography and embolization via direct puncture technique followed by excision of the mass via a combined transcervical and limited sternotomy approach.We describe an unusual case of vagal paraganglioma at the cervicothoracic junction with retrosternal extension requiring a sternotomy for surgical excision.© 2023 Wiley Periodicals LLC.