血管肉瘤，也被称为恶性血管内皮瘤，是一种罕见的血管源性恶性肿瘤，常见于头颈部的皮肤，极少发生在颅内区域。至于颅内脑膜血管肉瘤，之前只报告了8例，并且没有大样本的临床研究。我们在此报告一例幕间痉孪脑膜血管肉瘤病例。一名48岁的中国男性患者因头痛合并双下肢无力入院。入院时，CT显示位于额叶顶部侧脑窦两侧的高密度肿块。我们进行了肿瘤的探查性手术切除。手术过程中发现肿瘤起源于硬脑膜，并广泛浸润周围脑组织和颅骨，观察到周围的血斑铁沉积。术后病理学提示为血管肉瘤。颅内脑膜血管肉瘤在手术前很难准确诊断，因此放射科医师和神经外科医师需要加强对该疾病的了解。手术过程中存在广泛的表浅血斑铁沉积可能有助于诊断，并且免疫组化在颅内血管肉瘤的诊断中非常重要。© 2023. BioMed Central Ltd., part of Springer Nature.

Angiosarcoma, also known as malignant hemangioendothelioma, is a rare vasogenic malignant tumor, commonly found on the skin of the head and neck, rarely occurring in the intracranial region. As for intracranial meningeal angiosarcoma, only 8 cases have been reported before and there is no clinical study with large sample size. We report here a case of parasagittal meningeal angiosarcoma.A 48-year-old Chinese male patient was admitted to our hospital due to headache accompanied by bilateral lower limb weakness. On admission, CT showed a high-density mass on both sides of the sagittal sinus at the top of the frontal lobe. We performed exploratory surgical resection of the tumor. During the operation, it was found that the tumor originated from the dura mater and extensively invaded the surrounding brain tissue and skull, and the surrounding hemosiderin deposition was observed. Postoperative pathology suggested angiosarcoma.Intracranial meningeal angiosarcoma is difficult to accurately diagnose before surgery, so radiologists and neurosurgeons need to strengthen their understanding of this disease. The presence of extensive superficial hemosiderin deposition during operation may contribute to the diagnosis, and immunohistochemistry is very important for the diagnosis of intracranial angiosarcoma.© 2023. BioMed Central Ltd., part of Springer Nature.