儿童巨大囊性实性颅咽管瘤（CP），在CP腔内植入Ommaya储液器，并在肿瘤切除前持续引流囊液5天。 一名11岁男性患者因肿瘤入院。至视力丧失1年，间歇性头痛、呕吐6个月，尿频2个月。此外，头部磁共振检查显示鞍区、鞍上及双侧额叶囊性实性病变，大小为96.0×82.6×76.0 mm。在手术切除之前，将 Ommaya 储库植入肿瘤腔内。引流持续 5 天，引流量为 39 至 50 mL（43.80 ± 4.67 mL）。肿瘤缩小后，进行了开颅手术。手术治疗后，CP被完全切除。孩子随后出现甲状腺功能减退症和皮质醇功能减退症，并接受激素替代疗法。随访3年未见肿瘤复发。儿童巨大囊性实性CP的治疗具有挑战性。术前植入 Ommaya 储库、持续引流囊液、缩小肿瘤、降低肿瘤张力有利于肿瘤切除。版权所有 © 2024 by Mutaz B. Habal, MD。

In children with giant cystic solid craniopharyngioma (CP), the Ommaya reservoir was implanted in the CP cavity, and the cystic fluid was continuously drained for 5 days before the tumor resection.An 11-year-old male patient was admitted to the hospital due to vision loss for 1 year, intermittent headache, vomiting for 6 months, and frequent urination for 2 months. Besides, magnetic resonance imaging of the head showed cystic solid lesions in the sellar region, suprasellar, and bilateral frontal lobes, with a size of 96.0×82.6×76.0 mm. Before the surgical resection, an Ommaya reservoir was implanted within the tumor cavity. The drainage was continued for 5 days and was 39 to 50 mL (43.80 ± 4.67 mL). Following the tumor shrank, a craniotomy was performed.Following surgical treatment, the CP was entirely removed. The child subsequently developed hypothyroidism and hypocortisolism, for which hormone replacement therapy was administered. No tumor recurrence was observed after 3 years of follow-up.The treatment of giant cystic solid CP in children is challenging. Preoperative implantation of the Ommaya reservoir, continuous drainage of cystic fluid, shrinkage of the tumor, and reduction of tumor tension are beneficial for tumor resection.Copyright © 2024 by Mutaz B. Habal, MD.